Abernethy畸形致下消化道出血的診治_《中國普外基礎與臨床雜志》

作者：

 李震 ¹ , 汪忠鎬 ^1,2 , 趙克 ³ , 卞策 ³ , 韓冰 ³ , 郭巍 ³ , 崔琦 ³ , 霍小森 ¹ , 王雷永 ¹

1.中國航空工業中心醫院血管外科（北京 100012）;;
2.首都醫科大學血管外科研究所（北京 100053）;;
3.中國人民解放軍第二炮兵總醫院心胸血管外科（北京 100088）;

關鍵詞：

Abernethy畸形下消化道出血手術中藥

視頻：

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摘要 全文 圖表 視頻 參考文獻 施引文獻 補充材料

目的探討Abernethy畸形致下消化道出血的診斷及治療方法。
方法回顧1例Abernethy畸形患者的診治情況，并結合相關文獻進行分析。
結果血管造影確診后經積極術前準備，行剖腹探查、乙狀結腸造瘺術，術后3周開始給予中藥保留灌腸至術后7周，6個月關閉造瘺,3周后繼續輔以中藥保留灌腸4周。患者順利恢復出院，隨訪9個月未再次出血。
結論正確的診斷及合理的治療方案是救治的關鍵。

引用本文： 李震,汪忠鎬,趙克,卞策,韓冰,郭巍,崔琦,霍小森,王雷永. Abernethy畸形致下消化道出血的診治. 中國普外基礎與臨床雜志, 2010, 17(1): 83-84. doi: 復制

1.	Abernethy J. Account of two instances of uncommon formation in the viscera of the human body [Ｊ]. Phil Trans R Soc, 1793; 83: 5966.
2.	陳國庭, 李恒平. Abernethy畸形一例 [Ｊ]. 中華普通外科雜志, 2005; 20(5): 328.
3.	陳誠豪, 王大勇, 李小松, 等. 先天性肝外門腔靜脈分流并下消化道出血1例 [Ｊ]. 臨床小兒外科雜志, 2007; 6(2): 7879.
4.	Murray CP, Yoo SJ, Babyn PS. Congenital extrahepatic portosystemic shunts [Ｊ]. Pediatr Radiol, 2003; 33(9): 614620.
5.	Kumar A, Kumar J, Aggarwal R, et al. Abernethy malformation with portal vein aneurysm [Ｊ]. Diagn Interv Radiol, 2008; 14(3): 143146.
6.	Oei M, Wessling J. Abernethy malformation-congenital aplasia of the portal vein a 29yearold patient [Ｊ]. Rofo, 2007; 179(2): 167169.
7.	Abernethy LJ. Classification and imaging of vascular malformations in children [Ｊ]. Eur Radiol, 2003; 13(11): 24832497.
8.	Howard ER, Davenport M. Congenital extrahepatic portocaval shuntsthe Abernethy malformation (Review) [Ｊ]. J Pediatr Surg, 1997; 32(3): 494497.
9.	Moon SB, Park KW, Jung SE. Abnormal direct entry of the umbilical vein into the portal vein: report of a case [Ｊ]. Pediatr Surg Int, 2008; 24(11): 12431245.
10.	Ringe K, Schirg E, Melter M, et al. Congenital absence of the portal vein (CAPV). Two cases of Abernethy malformation type 1 and review of the literature [Ｊ]. Radiologe, 2008; 48(5): 493502.
11.	Witters P, Maleux G, George C, et al. Congenital venovenous malformations of the liver: widely variable clinical presentations [Ｊ]. J Gastroenterol Hepatol, 2008; 23(8 Pt 2): e390e394.
12.	Stringer MD. The clinical anatomy of congenital portosystemic venous shunts [Ｊ]. Clin Anat, 2008; 21(2): 147157.
13.	Morikawa N, Honna T, Kuroda T, et al. Resolution of hepatopulmonary syndrome after ligation of a portosystemic shunt in a pediatric patient with an Abernethy malformation [Ｊ]. J Pediatr Surg, 2008; 43(2): e35e38.
14.	Emre S, Arnon R, Cohen E, et al. Resolution of hepatopulmonary syndrome after auxiliary partial orthotopic liver transplantation in Abernethy malformation. A case report [Ｊ]. Liver Transpl, 2007; 13(12): 16621668.
15.	吳繼東, 汪忠鎬, 王仕華, 等. 兒童肝外型門脈高壓癥的診治 [Ｊ]. 中國現代手術學雜志, 2003; 7(5): 375377.
16.	王欣博, 童中勛, 劉威, 等. 門靜脈海綿樣變性外科治療的研究進展 [Ｊ]. 中國普外基礎與臨床雜志， 2008; 15(12): 877879.
17.	蓋保東, 王正峰, 劉東. 門脈高壓性胃病 [Ｊ]. 中國普外基礎與臨床雜志, 2008; 15(12): 880882.
18.	Tercier S, Delarue A, Rouault F, et al. Congenital portocaval fistula associated with hepatopulmonary syndrome: ligation vs liver transplantation[Ｊ]. J Pediatr Surg, 2006; 41(2): e1e3.

1. Abernethy J. Account of two instances of uncommon formation in the viscera of the human body [Ｊ]. Phil Trans R Soc, 1793; 83: 5966.
2. 陳國庭, 李恒平. Abernethy畸形一例 [Ｊ]. 中華普通外科雜志, 2005; 20(5): 328.
3. 陳誠豪, 王大勇, 李小松, 等. 先天性肝外門腔靜脈分流并下消化道出血1例 [Ｊ]. 臨床小兒外科雜志, 2007; 6(2): 7879.
4. Murray CP, Yoo SJ, Babyn PS. Congenital extrahepatic portosystemic shunts [Ｊ]. Pediatr Radiol, 2003; 33(9): 614620.
5. Kumar A, Kumar J, Aggarwal R, et al. Abernethy malformation with portal vein aneurysm [Ｊ]. Diagn Interv Radiol, 2008; 14(3): 143146.
6. Oei M, Wessling J. Abernethy malformation-congenital aplasia of the portal vein a 29yearold patient [Ｊ]. Rofo, 2007; 179(2): 167169.
7. Abernethy LJ. Classification and imaging of vascular malformations in children [Ｊ]. Eur Radiol, 2003; 13(11): 24832497.
8. Howard ER, Davenport M. Congenital extrahepatic portocaval shuntsthe Abernethy malformation (Review) [Ｊ]. J Pediatr Surg, 1997; 32(3): 494497.
9. Moon SB, Park KW, Jung SE. Abnormal direct entry of the umbilical vein into the portal vein: report of a case [Ｊ]. Pediatr Surg Int, 2008; 24(11): 12431245.
10. Ringe K, Schirg E, Melter M, et al. Congenital absence of the portal vein (CAPV). Two cases of Abernethy malformation type 1 and review of the literature [Ｊ]. Radiologe, 2008; 48(5): 493502.
11. Witters P, Maleux G, George C, et al. Congenital venovenous malformations of the liver: widely variable clinical presentations [Ｊ]. J Gastroenterol Hepatol, 2008; 23(8 Pt 2): e390e394.
12. Stringer MD. The clinical anatomy of congenital portosystemic venous shunts [Ｊ]. Clin Anat, 2008; 21(2): 147157.
13. Morikawa N, Honna T, Kuroda T, et al. Resolution of hepatopulmonary syndrome after ligation of a portosystemic shunt in a pediatric patient with an Abernethy malformation [Ｊ]. J Pediatr Surg, 2008; 43(2): e35e38.
14. Emre S, Arnon R, Cohen E, et al. Resolution of hepatopulmonary syndrome after auxiliary partial orthotopic liver transplantation in Abernethy malformation. A case report [Ｊ]. Liver Transpl, 2007; 13(12): 16621668.
15. 吳繼東, 汪忠鎬, 王仕華, 等. 兒童肝外型門脈高壓癥的診治 [Ｊ]. 中國現代手術學雜志, 2003; 7(5): 375377.
16. 王欣博, 童中勛, 劉威, 等. 門靜脈海綿樣變性外科治療的研究進展 [Ｊ]. 中國普外基礎與臨床雜志， 2008; 15(12): 877879.
17. 蓋保東, 王正峰, 劉東. 門脈高壓性胃病 [Ｊ]. 中國普外基礎與臨床雜志, 2008; 15(12): 880882.
18. Tercier S, Delarue A, Rouault F, et al. Congenital portocaval fistula associated with hepatopulmonary syndrome: ligation vs liver transplantation[Ｊ]. J Pediatr Surg, 2006; 41(2): e1e3.

《中國普外基礎與臨床雜志》

Abernethy畸形致下消化道出血的診治

摘要 全文 圖表 視頻 參考文獻 施引文獻 補充材料

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《中國普外基礎與臨床雜志》

Abernethy畸形致下消化道出血的診治

摘要 全文 圖表 視頻 參考文獻 施引文獻 補充材料

Format

Content

摘要全文圖表視頻參考文獻施引文獻補充材料